Reaction Details

Stochiometric Equation O2 + 2-Oxoglutarate + 4-Trimethylammoniobutanoate <-> CO2 + Succinate + Carnitine
Substrates
O2
2-Oxoglutarate
4-Trimethylammoniobutanoate
Products
CO2
Succinate
Carnitine
Enzymes known to catalyse this reaction (curated information)
EC Numberin OrganismUniProt LinkPubMedID
1.14.11.1 Homo sapiens UniProt 6497835
Pathways Lysine degradation
Metabolic pathways


View all entries for reaction O2 + 2-Oxoglutarate + 4-Trimethylammoniobutanoate <-> CO2 + Succinate + Carnitine