Reaction Details

Stochiometric Equation O2 + 2-Oxoglutarate + 4-Trimethylammoniobutanoate <-> CO2 + L-Carnitine + Succinate
Substrates
O2
2-Oxoglutarate
4-Trimethylammoniobutanoate
Products
L-Carnitine
CO2
Succinate
Enzymes known to catalyse this reaction (curated information)
EC Numberin OrganismUniProt LinkPubMedID
1.14.11.1 Rattus norvegicus UniProt 3378057
Pathways Lysine degradation


View all entries for reaction O2 + 2-Oxoglutarate + 4-Trimethylammoniobutanoate <-> CO2 + L-Carnitine + Succinate